AGSD-UK Conference 2010

The Conference will be in central London on weekend of 20th-21st November. More details soon.

 

Walk over Wales... every step counts
2 July to 2 August 2010
Sponsored walk raising money for AGSD-UK. 210 miles. Details.

 

Walking with McArdle's - Wales
An opportunity to enjoy a week's walking holiday in Snowdonia and learn how best to cope with McArdle's. July 2011. Details.

 

 


 

AGSD-UK Conference 2010

The Conference will be in central London on weekend of 20th-21st November. More details soon.

 

Walk over Wales... every step counts
2 July to 2 August 2010
Sponsored walk raising money for AGSD-UK. 210 miles. Details.

 

Walking with McArdle's - Wales
An opportunity to enjoy a week's walking holiday in Snowdonia and learn how best to cope with McArdle's. July 2011. Details.

 

 

Glycogen Storage Disease Type III

Also known as Cori disease or debrancher enzyme deficiency.

Children with GSD III are often first diagnosed because they have been noticed to have a swollen abdomen due to a very large liver. Some children have problems with low blood sugars on fasting but this is not as common as in GSD I.

Growth may be delayed during childhood but the majority attain a normal final adult height. Although some older individuals develop problems with muscle weakness (which may also affect the heart), the outcome for most is good with the liver returning to a normal size with age.

 

Type III summary
Symptoms Swollen abdomen, low blood sugars on fasting
(for some), growth delayed during childhood
Secondary symptoms Problems with muscle weakness
Treatment See below
Outlook Good, with the liver returning to a normal
size with age

 

Glycogen Storage Disease Type III

Also known as Cori disease or debrancher enzyme deficiency.

Children with GSD III are often first diagnosed because they have been noticed to have a swollen abdomen due to a very large liver. Some children have problems with low blood sugars on fasting but this is not as common as in GSD I.

Growth may be delayed during childhood but the majority attain a normal final adult height. Although some older individuals develop problems with muscle weakness (which may also affect the heart), the outcome for most is good with the liver returning to a normal size with age.

 

Type III summary
Symptoms Swollen abdomen, low blood sugars on fasting
(for some), growth delayed during childhood
Secondary symptoms Problems with muscle weakness
Treatment See below
Outlook Good, with the liver returning to a normal
size with age